Department of Cardiothoracic Surgery, Faculty of Medical Science, Lebanese University, Beirut, Lebanon; Department of Cardiothoracic Surgery, Lebanese Geitaoui University Hospital, Beirut, Lebanon;. Electronic address: [Email]
Malignant peripheral nerve sheath tumors (MPNST), also known as malignant schwannoma, are rare soft tissue sarcomas . They commonly invade axial sites and rarely do they occur in the thorax . Herein, we present the case of an enormous metastatic multilobulated intrathoracic MPNST that was first misdiagnosed as desmoid fibromatosis and successfully resected for palliative purpose.